Strategic Partners A/S — Major Shareholding Notification 2023

May 9, 2023

ORPHAZYME

Company announcement
No. 04/2023

Orphazyme A/S
Ole Maaløes Vej 3
DK-2200 Copenhagen N
www.orphazyme.com
Company Registration No. 32266355

Major shareholder announcement

Copenhagen, Denmark, May 9, 2023 – Orphazyme A/S (ORPHA.CO) (the "Company"), hereby announces the receipt of notification pursuant to Section 38 of the Danish Capital Markets Act from MH Investment ApS, that as of May 8, 2023, MH Investment ApS holds shares, corresponding to more than 5% of the total share capital and voting rights in the Company.

For additional information, please contact

Orphazyme A/S
Anders Vadsholt, Chief Executive Officer and Chief Financial Officer: +45 28 98 90 55

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