Strategic Partners A/S — Major Shareholding Notification 2023

May 17, 2023

ORPHAZYME

Company announcement
No. 09/2023

Orphazyme A/S
Ole Maaløes Vej 3
DK-2200 Copenhagen N
www.orphazyme.com
Company Registration No. 32266355

Major shareholder announcement

Copenhagen, Denmark, May 17, 2023 – Orphazyme A/S (ORPHA.CO) (the "Company"), hereby announces the receipt of notification pursuant to Section 38 of the Danish Capital Markets Act from MH Investment ApS, that as of May 16, 2023, MH Investment ApS holds shares corresponding to 10.00% of the total share capital and voting rights in the Company.

For additional information, please contact
Orphazyme A/S
Michael Hove, Chairman of the board +45 28 12 66 09

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