Strategic Partners A/S — Major Shareholding Notification 2023

May 19, 2023

ORPHAZYME

Company announcement
No. 10/2023

Orphazyme A/S
Ole Maaløes Vej 3
DK-2200 Copenhagen N
www.orphazyme.com
Company Registration No. 32266355

Major shareholder announcement

Copenhagen, Denmark, May 19, 2023 – Orphazyme A/S (ORPHA.CO) (the "Company"), hereby announces the receipt of notification pursuant to Section 38 of the Danish Capital Markets Act from Scandinavian Investment Group A/S, that as of May 16, 2023, Scandinavian Investment Group A/S holds shares corresponding to 10.00% of the total share capital and voting rights in the Company.

For additional information, please contact
Orphazyme A/S
Michael Hove, Chairman of the board +45 28 12 66 09

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